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CLC number: R745.4+3

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Received: 2005-08-03

Revision Accepted: 2005-11-13

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Journal of Zhejiang University SCIENCE B 2006 Vol.7 No.2 P.138-141


A case of overlapping Bickerstaff’s brainstem encephalitis and Guillain-Barré syndrome

Author(s):  Wang De-sheng, Tang Ying, Wang Ye

Affiliation(s):  Department of Neurology, the First Hospital of Harbin Medical University, Harbin 150001, China; more

Corresponding email(s):   hydtangying@hotmail.com

Key Words:  Bickerstaff&rsquo, s brainstem encephalitis, Fisher syndrome, Guillain-Barré, syndrome

Wang De-sheng, Tang Ying, Wang Ye. A case of overlapping Bickerstaff’s brainstem encephalitis and Guillain-Barré syndrome[J]. Journal of Zhejiang University Science B, 2006, 7(2): 138-141.

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author="Wang De-sheng, Tang Ying, Wang Ye",
journal="Journal of Zhejiang University Science B",
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%T A case of overlapping Bickerstaff’s brainstem encephalitis and Guillain-Barré syndrome
%A Wang De-sheng
%A Tang Ying
%A Wang Ye
%J Journal of Zhejiang University SCIENCE B
%V 7
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%P 138-141
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%D 2006
%I Zhejiang University Press & Springer
%DOI 10.1631/jzus.2006.B0138

T1 - A case of overlapping Bickerstaff’s brainstem encephalitis and Guillain-Barré syndrome
A1 - Wang De-sheng
A1 - Tang Ying
A1 - Wang Ye
J0 - Journal of Zhejiang University Science B
VL - 7
IS - 2
SP - 138
EP - 141
%@ 1673-1581
Y1 - 2006
PB - Zhejiang University Press & Springer
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DOI - 10.1631/jzus.2006.B0138

Objective: There is no report on bickerstaff&rsquo;s brainstem encephalitis (BBE) patients in China. We here report the first case of BBE in China. Methods: Clinical features, results of electromyography, electroencephalography (EEG), magnetic resonance imaging (MRI) and cerebrospinal fluid (CSF) examination were studied to clarify the characteristics of this syndrome. Results: A 44-year-old man presented himself at our inpatient department with somnolence and dizziness as his initial symptoms. He developed multiple cranial nerves paralysis especially internal and external ophthalmoplegia, ataxia and tetraparesis within 1 week. His condition rapidly deteriorated, and he experienced coma. Electromyography showed indications of peripheral nerve dysfunction, electroencephalography revealed loss of basic rhythm, MRI demonstrated high-intensity abnormalities on T2-weighted images of medulla oblongata, and CSF albuminocytological dissociation was defined abnormally as high protein. Ten months later, he almost completely recovered. Conclusion: BBE, syndrome%29&ck%5B%5D=abstract&ck%5B%5D=keyword'>fisher syndrome (FS) and guillain-Barré; syndrome (GBS) are similar clinically; BBE and FS were proposed to be the variant of GBS.

Darkslateblue:Affiliate; Royal Blue:Author; Turquoise:Article


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